[1]曲腾飞,宋晓峰,马广涛,等.腹膜后CASTLEMAN病伴副肿瘤性天疱疮1例报道并文献复习[J].齐鲁医学杂志,2017,32(03):263-264,269.[doi:10.13362/j.qlyx.201703004]
 QU Tengfei,SONG Xiaofeng,MA Guangtao,et al.ONE CASE OF RETROPERITONEAL CASTLEMAN DISEASE COMPLICATED BY PARANEOPLASTIC PEMPHIGUS AND LITERATURE REVIEW[J].Medical Journal of Qilu,2017,32(03):263-264,269.[doi:10.13362/j.qlyx.201703004]
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腹膜后CASTLEMAN病伴副肿瘤性天疱疮1例报道并文献复习()
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《齐鲁医学杂志》[ISSN:1008-0341/CN:37-1280/R]

卷:
第32卷
期数:
2017年03期
页码:
263-264,269
栏目:
出版日期:
2017-08-07

文章信息/Info

Title:
ONE CASE OF RETROPERITONEAL CASTLEMAN DISEASE COMPLICATED BY PARANEOPLASTIC PEMPHIGUS AND LITERATURE REVIEW
文章编号:
1008-0341(2017)03-0263-03
作者:
曲腾飞1宋晓峰1马广涛1于才艳2邱法波1
青岛大学附属医院,山东 青岛 266003 1 肝胆胰腺外科; 2 急诊普外科
Author(s):
QU Tengfei SONG Xiaofeng MA Guangtao YU Caiyan QIU Fabo
Department of Hepatopancreato Biliary Surgery, The Affiliated Hospital of Qingdao University, Qingdao 266003, China
关键词:
腹膜后肿瘤巨淋巴结增生副肿瘤综合征诊断
Keywords:
retroperitoneal neoplasms Giant Lymph Node Hyperplasia paraneoplastic syndromes diagnosis
分类号:
R733.4
DOI:
10.13362/j.qlyx.201703004
文献标志码:
A
摘要:
目的 探讨腹膜后CASTLEMAN病(RPCD)伴副肿瘤性天疱疮(PNP)的特点及诊治经验。
方法 回顾性分析我院诊治的1例RPCD伴PNP病人的临床资料,并查阅相关文献进行复习。
结果 病人为33岁男性,以口腔天疱疮为首发症状,糖皮质激素治疗效果不佳,口腔黏膜活检病理检查示天疱疮。盆腔增强CT检查提示腹膜后占位性病变,行开腹手术,术后病理检查提示RPCD,术后天疱疮症状逐渐减轻。
结论 该病罕见,其诊断常被延误,手术是治疗该病的根本方法,但术后皮肤黏膜症状可持续较长时间。
Abstract:
Objective  To investigate the features of retroperitoneal CASTLEMAN disease (RPCD) complicated by paraneoplastic pemphigus (PNP) and related diagnosis and treatment experience.
Methods  A retrospective analysis was performed for the clinical data of one patient with RPCD complicated by PNP who were diagnosed and treated in our hospital, and literature review was also performed.
Results  The patient was a 33-year-old man with an initial symptom of oral pemphigus and had poor response to glucocorticoids. Oral mucosal biopsy showed pemphigus. Pelvic contrast-enhanced computed tomography showed a retroperitoneal space-occupying lesion. An open surgery was performed and postoperative pathological examination suggested RPCD. The symptom of pemphigus was gradually alleviated after surgery.
Conclusion  This disease is rare and its diagnosis is often delayed. Surgery is the radical treatment of this disease, but skin and mucosal symptoms may last for a long time after surgery.
更新日期/Last Update: 2017-08-12